Antiphospholipid syndrome thiab cev xeeb tub

Antiphospholipid Syndrome (APS) yog ib hom mob autoimmune ntshawv siab uas yog tsim los ntawm kev tsim muaj ntau hom tshuaj tiv thaiv rau phospholipids nyob rau hauv cov ntshav ntshav (antiphospholipid antibodies). Ntawm cov poj niam uas mob ntawm txoj kev tuaj yeem , cov xwm txheej ntawm cov tshuaj antiphospholipid syndrome yog siab, thiab yog 28-43%. Qhov teeb meem loj ntawm no pathology yog thrombosis.

Vim li cas tseem ceeb rau kev tsim txoj cai APS?

Qhov ua rau ntawm txoj kev loj hlob ntawm antiphospholipid syndrome yog tsawg. Tus mob pathology no tuaj yeem tsim muaj rau hauv cov nram qab no:

  1. Thaum ib tug poj niam mob nrog mob lupus erythematosus .
  2. Muaj nyob rau hauv lub anamnesis ntawm ib tug thrombosis. Thaum cov hlab ntsha hauv plab uas muab ntshav rau txoj hnyuv, qhov kev sib tw "plab hlaub" pib tshwm, uas yog qhov tshwm sim los ntawm qhov pom ntawm qhov muag, tswj kev mob nkeeg hauv thaj tsam plab tam sim ntawd tom qab noj tshuaj.
  3. Txo cov platelets nyob rau hauv cov ntshav, uas tsis nrog los ntawm cov kev mob tshwm sim.
  4. Qhov kuaj pom ntawm keeb kwm ntawm myocardial infarction thiab lwm yam kab mob nrog rau kev mob plawv mob ntshav.

Tus mob antiphospholipid syndrome no tshwm sim li cas?

Cov tsos mob ntawm tus mob antiphospholipid syndrome, ncaj qha nyob ntawm ntau yam. Yog li tseem ceeb heev yog cov nram qab no nta:

Yog li, nyob rau hauv rooj plaub thaum muaj ib qho blockage ntawm cov hlab ntsha me me, raug teeb meem ntawm kev ua txhaum ntawm lub koom haum uas txuam rau lawv raug pom. Piv txwv li, yog hais tias qhov chaw ntawm cov vascular reticulums me ntsis, muaj kev ua txhaum ntawm kev mob ntawm cov leeg ntawm myocardium, tab sis yog hais tias lub lumen ntawm lub coronary artery raug kaw, tus mob myocardial infarction yuav tshwm sim.

Feem ntau cov antiphospholipid syndrome nyob rau hauv cov poj niam cev xeeb tub tau ntsi xws li ntau yam kab mob pathologies, uas yog cov tsos mob tib yam. Yog li, cov tsos mob ntawm cov tshuaj antiphospholipid syndrome tuaj yeem tshwm sim nyob rau hauv lub xub ntiag ntawm reticular lyvedo (lacy, thin mesh ntawm cov hlab ntsha ntawm daim tawv nqaij). Tsis tas li ntawd, ntev hlab ntsws ulcers, uas tsis yooj yim kho, thiab txawm tias peripheral gangrene, tuaj yeem qhia tias muaj cov kab mob no hauv lub cev.

Yuav kho li cas?

Kev kho mob ntawm antiphospholipid syndrome thaum cev xeeb tub yog ua raws li kev tswj ntawm ob tus kws kho mob: ib tus kws kho mob pojniam thiab tus kws kho mob. Qhov kev kho yooj yim ntawm no pathology yog siv cov glucocorticoids thiab cytostatics. Nrog ib lub ntsiab lus ntawm cov tshuaj tiv thaiv nyob rau hauv cov ntshav, tsuas yog kev daws teeb meem yog ua rau plasmapheresis (ntshav purification).