Addison tus kab mob ("bronze disease") yog ib qho kab mob tsawg kawg ntawm qhov kev tiv thaiv endocrine, thawj zaug tau piav nyob nruab nrab ntawm XIX xyoo los ntawm kws kho mob Askiv-kws kho mob T. Addison. Cov neeg uas muaj hnub nyoog li ntawm 20 xyoo thiab 50 xyoos feem ntau yog cov uas raug rau tus kab mob. Ua li cas rau hauv lub cev nrog no pathology, dab tsi yog qhov ua rau nws tshwm sim thiab niaj hnub txoj kev kho mob, peb yuav xav txog ntxiv.
Addison tus kab mob - etiology thiab pathogenesis
Addison tus kab mob yog tshwm sim los ntawm kev puas tsuaj ob sab rau lub qog nqaij cathex. Hauv qhov no, yuav txo tau lossis ua kom tiav cov khoom xyaw ntawm cov tshuaj hormones, tshwj xeeb tshaj yog glucocorticoids (cortisone thiab hydrocortisone) tswj cov protein, carbohydrate thiab roj metabolism, thiab cov mineralocorticoids (deoxycorticosterone thiab aldosterone) kom tswj cov dej-ntsev cov metabolism.
Ib feem thib tsib ntawm cov mob ntawm tus kab mob no yog neeg tsis paub keeb kwm. Ntawm qhov paub ua rau ntawm Addison tus kab mob, peb tuaj yeem paub qhov txawv li nram qab no:
- otoimmune lesion ntawm cov cortex adrenal;
- AIDS;
- syphilis;
- adrenoleukodystrophy;
- tuberculosis ntawm qog adrenal;
- amyloidosis ;
- sarcoidosis;
- tshem tawm cov qog ntawm qog;
- hemorrhages nyob rau hauv qog adrenal;
- mus sij hawm ntev kho nrog cov tshuaj hormones;
- fungal qhov quav.
Ib qho kev txo qis rau hauv cov pob zeb qhuav tuaj yeem ua rau lub cev poob ntawm lub cev, lub cev tsis muaj zog, thiab lub ntim ntawm cov ntshav thiab lwm cov kev ua haujlwm kuj yuav txo tau. Qhov tsis muaj synthesis ntawm glucocorticoids ua rau cov kev ua txhaum ntawm carbohydrate metabolism, ib tug poob rau hauv cov ntshav qab zib, thiab vascular insufficiency.
Cov tsos mob ntawm tus kab mob Adison
Raws li txoj cai, txoj kev loj hlob ntawm Addison tus kab mob tshwm sim qeeb qeeb, txij li ob peb lub hlis mus rau ob peb lub xyoos, thiab nws cov tsos mob feem ntau mus tsis paub ntev ntev. Tus kabmob no tuaj yeem tshwm sim thaum lub cev muaj mob hnyav rau glucocorticoids, uas tuaj yeem txuam nrog kev ntxhov siab lossis kev mob ntsws.
Cov tsos mob ntawm tus kab mob no muaj xws li:
- ceev ceev qaug zog;
- leeg tsis muaj zog;
- tsis nco;
- poob phaus;
- cuam tshuam ntawm txoj hnyuv quav;
- ntshav siab;
- hyperpigmentation ntawm daim tawv nqaij (me ntsis ntawm cov xim bronze) - tshwm sim ntev ua ntej cov tsos mob ntawm lwm cov tsos mob;
- Attraction rau salty thiab qaub zaub mov;
- nqhis dej;
- cev tsis ntiav;
- tremor ntawm txhais tes , lub taub hau;
- tshaj zis;
- tachycardia thiab lwm tus.
Addisonian ntsoog
Yog hais tias cov tsos mob ntawm tus kab mob no tshwm sim sai sai, muaj tus kab mob adrenocortical insufficiency tshwm sim. Qhov mob no hu ua "addisonian crisis" thiab yog lub neej txoj sia. Nws tshwm sim nws tus kheej los ntawm tej yam xws li mob hnyav heev hauv qis qis, lub plab lossis ceg, ntuav ntuav thiab zawv plab, tsis nco qab, nplaig xim ntawm tus nplaig, thiab lwm yam.
Addison tus kab mob - mob
Yog hais tias Addison tus kab mob xav tias, kuaj kev kuaj xyuas tau ua kom pom tau tias txo qis hauv sodium ntau ntau thiab potassium, txo qis hauv cov ntshav qabzib, cov ntsiab lus qis hauv cov ntshav, cov ntsiab lus ntawm eosinophils, thiab lwm tus.
Addison tus kab mob - kev kho mob
Cov kev kho mob ntawm tus kab mob yog raws li tshuaj hloov chaw tshuaj hormone therapy. Raws li txoj cai, qhov tsis muaj cortisol hloov los ntawm hydrocortisone, thiab tsis muaj cov ntxhuav corticosteroid
Nrog Addison cov teebmeem, cov kabmob glaucocorticoids thiab cov cim tagnrho ntawm cov kua roj saline nrog cov dextrose muaj kws kho mob, uas tso cai rau kev kho mob thiab tshem tawm cov kev hem thawj ntawm lub neej.
Kev kho mob yuav tsum muaj kev noj haus uas txwv tsis pub cov nqaij thiab cov cais tawm cov qos yaj ywm, cov khoom qab zib, txiv ntseej, tsawb (kom tsis txhob noj cov kua qaub). Qhov kev noj haus ntawm cov ntsev, cov carbohydrates thiab cov vitamins, tshwj xeeb tshaj yog C thiab B, yog nce ntxiv. Qhov kev ntsuam xyuas nrog kev tsim nyog thiab sij hawm kho tus mob Addison tau zoo heev.